Pathogenesis of paroxysmal nocturnal hemoglobin uria.
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論文 (290件):
Yicheng Wang, Taroh Kinoshita. The role of lipid scramblases in regulating lipid distributions at cellular membranes. Biochemical Society transactions. 2023
Shu-Ya Cao, Yi-Shi Liu, Xiao-Dong Gao, Taroh Kinoshita, Morihisa Fujita. A lipid scramblase TMEM41B is involved in the processing and transport of GPI-anchored proteins. Journal of biochemistry. 2023. 174. 2. 109-123
Yi-Shi Liu, Yicheng Wang, Xiaoman Zhou, Linpei Zhang, Ganglong Yang, Xiao-Dong Gao, Yoshiko Murakami, Morihisa Fujita, Taroh Kinoshita. Accumulated precursors of specific GPI-anchored proteins upregulate GPI biosynthesis with ARV1. The Journal of cell biology. 2023. 222. 5
Atsushi Kobayashi, Tetsuya Hirata, Taishi Shimazaki, Yoshiko Munesue, Keisuke Aoshima, Takashi Kimura, Junko Nio-Kobayashi, Rie Hasebe, Atsuko Takeuchi, Yuichi Matsuura, et al. A point mutation in GPI-attachment signal peptide accelerates the development of prion disease. Acta neuropathologica. 2023. 145. 5. 637-650
Jun-Ichi Nishimura, Antoine Soubret, Noriko Arase, Simon Buatois, Masaki Hotta, Jean-Eric Charoin, Yoshikazu Ito, Sasha Sreckovic, Hiroyuki Takamori, Christoph Bucher, et al. Mitigating Drug-Target-Drug Complexes in Patients With Paroxysmal Nocturnal Hemoglobinuria Who Switch C5 Inhibitors. Clinical pharmacology and therapeutics. 2023. 113. 4. 904-915