文献
J-GLOBAL ID:201802210579815852
整理番号:18A0719196
角膜ジストロフィー変異は潜在的アミロイド形成ドメインにおけるTGF2P安定性と溶解性を標的とすることにより病原性を駆動する【JST・京大機械翻訳】
Corneal Dystrophy Mutations Drive Pathogenesis by Targeting TGFBIp Stability and Solubility in a Latent Amyloid-forming Domain
著者 (11件):
Stenvang Marcel
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Schafer Nicholas P.
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Malmos Kirsten Gade
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Perez Adriana-Michelle Wolf
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Niembro Olatz
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Sormanni Pietro
(Department of Chemistry, University of Cambridge, Cambridge, CB2 1EW, United Kingdom)
,
Basaiawmoit Rajiv Vaid
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Christiansen Gunna
(Department of Biomedicine, Aarhus University, Aarhus, Denmark)
,
Andreasen Maria
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
,
Andreasen Maria
(Department of Biomedicine, Aarhus University, Aarhus, Denmark)
,
Otzen Daniel E.
(Interdisciplinary Nanoscience Center (iNANO), Department of Molecular Biology, Aarhus University, 8000 Aarhus C, Denmark)
資料名:
Journal of Molecular Biology
(Journal of Molecular Biology)
巻:
430
号:
8
ページ:
1116-1140
発行年:
2018年
JST資料番号:
D0124B
ISSN:
0022-2836
資料種別:
逐次刊行物 (A)
記事区分:
原著論文
発行国:
オランダ (NLD)
言語:
英語 (EN)