文献
J-GLOBAL ID:201902271358359705
整理番号:19A0790758
一次胆汁酸合成欠損に対するコール酸:成人における好ましい転帰を可能にする救命療法【JST・京大機械翻訳】
Cholic acid for primary bile acid synthesis defects: a life-saving therapy allowing a favorable outcome in adulthood
著者 (18件):
Gonzales Emmanuel
(Pediatric Hepatology and Pediatric Liver Transplantation Unit, National Reference Centre for rare pediatric liver diseases and Filfoie, Hopital Bicetre, Assistance Publique-Hopitaux de Paris, Paris, France)
,
Gonzales Emmanuel
(Faculty of Medicine Paris - Sud, University Paris - Sud / Paris - Saclay, Paris, France)
,
Gonzales Emmanuel
(INSERM UMR-S1174 and Hepatinov, University Paris -Sud / Paris - Saclay, Orsay, France)
,
Gonzales Emmanuel
(Service d’Hepatologie et de Transplantation Hepatique Pediatriques, Hopital Bicetre, Le Kremlin-Bicetre, France)
,
Matarazzo Lorenza
(University of Trieste, Trieste, Italy)
,
Franchi-Abella Stephanie
(Faculty of Medicine Paris - Sud, University Paris - Sud / Paris - Saclay, Paris, France)
,
Franchi-Abella Stephanie
(Pediatric Radiology Unit, Hopital Bicetre, Assistance Publique - Hopitaux de Paris, Paris, France)
,
Dabadie Alain
(Department of Pediatrics, Hopital Sud, Rennes, France)
,
Cohen Joseph
(Pediatric Hepatology and Pediatric Liver Transplantation Unit, National Reference Centre for rare pediatric liver diseases and Filfoie, Hopital Bicetre, Assistance Publique-Hopitaux de Paris, Paris, France)
,
Habes Dalila
(Pediatric Hepatology and Pediatric Liver Transplantation Unit, National Reference Centre for rare pediatric liver diseases and Filfoie, Hopital Bicetre, Assistance Publique-Hopitaux de Paris, Paris, France)
,
Hillaire Sophie
(Hepatology Unit, Hopital Foch, and Hopital Beaujon, Assistance Publique - Hopitaux de Paris, Paris, France)
,
Guettier Catherine
(Faculty of Medicine Paris - Sud, University Paris - Sud / Paris - Saclay, Paris, France)
,
Guettier Catherine
(Pathology Unit, Hopital Bicetre, Assistance Publique - Hopitaux de Paris, Paris, France)
,
Taburet Anne-Marie
(Pharmacy Unit, Hopital Bicetre, Assistance Publique - Hopitaux de Paris, Paris, France)
,
Myara Anne
(Groupe Hospitalier Paris Saint-Joseph, Paris, France)
,
Jacquemin Emmanuel
(Pediatric Hepatology and Pediatric Liver Transplantation Unit, National Reference Centre for rare pediatric liver diseases and Filfoie, Hopital Bicetre, Assistance Publique-Hopitaux de Paris, Paris, France)
,
Jacquemin Emmanuel
(Faculty of Medicine Paris - Sud, University Paris - Sud / Paris - Saclay, Paris, France)
,
Jacquemin Emmanuel
(INSERM UMR-S1174 and Hepatinov, University Paris -Sud / Paris - Saclay, Orsay, France)
資料名:
Orphanet Journal of Rare Diseases (Web)
(Orphanet Journal of Rare Diseases (Web))
巻:
13
号:
1
ページ:
190
発行年:
2018年
JST資料番号:
U7532A
ISSN:
1750-1172
資料種別:
逐次刊行物 (A)
記事区分:
原著論文
発行国:
イギリス (GBR)
言語:
英語 (EN)