文献
J-GLOBAL ID:202202248559026052
整理番号:22A0894034
E1ユビキチン活性化酵素(UBA1)の標的化はF508delと稀なミスフォールドCFTR変異体に対するエレキサカフター/テザカフター/イバカフターの有効性を改善する【JST・京大機械翻訳】
Targeting the E1 ubiquitin-activating enzyme (UBA1) improves elexacaftor/tezacaftor/ivacaftor efficacy towards F508del and rare misfolded CFTR mutants
著者 (9件):
Borgo Christian
(Department of Biomedical Sciences, University of Padova, Padova, Italy)
,
D’Amore Claudio
(Department of Biomedical Sciences, University of Padova, Padova, Italy)
,
Capurro Valeria
(UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy)
,
Tomati Valeria
(UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy)
,
Sondo Elvira
(UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy)
,
Cresta Federico
(Centro Fibrosi Cistica, IRCCS Istituto Giannina Gaslini, Genova, Italy)
,
Castellani Carlo
(Centro Fibrosi Cistica, IRCCS Istituto Giannina Gaslini, Genova, Italy)
,
Pedemonte Nicoletta
(UOC Genetica Medica, IRCCS Istituto Giannina Gaslini, Genova, Italy)
,
Salvi Mauro
(Department of Biomedical Sciences, University of Padova, Padova, Italy)
資料名:
Cellular and Molecular Life Sciences
(Cellular and Molecular Life Sciences)
巻:
79
号:
4
ページ:
192
発行年:
2022年
JST資料番号:
B0496A
ISSN:
1420-682X
CODEN:
CMLSFI
資料種別:
逐次刊行物 (A)
記事区分:
原著論文
発行国:
ドイツ (DEU)
言語:
英語 (EN)