1) Hebbel RP, Boogaerts MA, Eaton JW, Steinberg MH: Erythrocyte adherence to endothelium in sickle-cell anemia. A possible determinant of disease severity. N Engl J Med 302 : 992-995, 1980.
2) Wick TM, Moake JL, Udden MM, Eskin SG, Sears DA, McIntire LV: Unusually large von Willebrand factor multimers increase adhesion of sickle erythrocytes to human endothelial cells under controlled flow. J Clin Invest 80 : 905-910, 1987.
3) Kaul DK, Nagel RL, Chen D, Tsai HM: Sickle erythrocyte-endothelial interactions in microcirculation: the role of von Willebrand factor and implications for vasoocclusion. Blood 81 : 2429-2438, 1993.
5) Tsai HM, Nagel RL, Hatcher VB, Seaton AC, Sussman II: The high molecular weight form of endothelial cell von Willebrand factor is released by the regulated pathway. Br J Haematol 79 : 239-245, 1991.