文献

J-GLOBAL ID：201702222627611675   整理番号：17A0578890

房室ブロックを誘発する心臓刺激伝導系におけるヘパラン硫酸貯蔵

Heparan sulfate storage in the cardiac conduction system triggers atrioventricular block

著者 (10件)： Kato Rie (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Kato Rie (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Miyahara Hiroaki (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Kawano Tatsuya (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Matsuzuka Atsuko (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Matsuzuka Atsuko (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Noda Kimiko (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Izumi Tatsuro (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Izumi Tatsuro (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Izumi Tatsuro (Department of Pediatrics and Child Neurology, Nanao National Hospital, Nanao, Ishikawa 9268531, Japan)
資料名： Brain & Development  (Brain & Development)
巻： 39  号： 5  ページ： 418-421  発行年： 2017年05月 
JST資料番号： W0814A  ISSN： 0387-7604  資料種別： 逐次刊行物 (A)
記事区分： 原著論文  発行国： オランダ (NLD)  言語： 英語 (EN)

抄録/ポイント： 要約 目的:発作性房室(AV)ブロックの患者を臨床病理学的に...

シソーラス用語： ヒト ,...
準シソーラス用語： *発作性房室ブロック ,...

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著者キーワード (5件)： Sanfilippo syndrome ,  Long-surviving patient ,  Heparan sulfate ,  Cardiac conduction system ,  Atrioventricular block

分類 (2件)： 循環系の疾患  (GJ03000C) ,  中毒一般  (GD06010Q)

引用文献 (9件)：

• Pyeritz, R.E. Cardiovascular manifestations of heritable disorders of connective tissue. Prog Med Genet. 1983;5:191-302.
• Kurihara, M., Kumagai, K., Yagishita, S. Sanfilippo syndrome type C: a clinicopathological autopsy study of a long-term survivor. Pediatr Neurol. 1996;14:317-21.
• Misumi, I., Chikazawa, S., Ishitsu, T., Higuchi, S., Shimazu, T., Ikeda, C. et al, Atrioventricular block and diastolic dysfunction in a patient with sanfilippo C. Int Med. 2010;49:2313-6.
• Ribeiro, E.R., Brusius-Facchin, A.C., Leistner-Segal, S., Bruno da Silva, C.A., Schwartz, I.V. Cardiac disease as the presenting feature of mucopolysaccharidosis type IIIA: a case report. Mol Genet Metab Rep. 2014;1:422-4.
• Shibata, S., Harpel, P., Bona, C., Fillit, H. Monoclonal antibodies to heparan sulfate inhibit the formation of thrombin-antithrombin III complexes. Clin Immunol Immunopathol. 1993;67:264-72.

タイトルに関連する用語 (5件)： 房室ブロック ,  誘発 ,  心臓刺激伝導系 ,  ヘパラン硫酸 ,  貯蔵