Art

J-GLOBAL ID：200902226695148321   Reference number：08A1214383

Effect of dietary Lorenzo’s oil and docosahexaenoic acid treatment for Zellweger syndrome

ツェルベーガー症候群における食餌性ロレンツォ油とドコサヘキサエン酸治療の影響

Author (7)： ARAI Yasuhiro (Juntendo Univ.) ,  ARAI Yasuhiro (Tokyo Metropolitan Tobu Medical Center for Persons with Developmental/Multiple Disabilities) ,  KITAMURA Yohei (Morinaga Milk Ind., Kanagawa, JPN) ,  HAYASHI Masaharu (Tokyo Metropolitan Inst. for Neuroscience) ,  OSHIDA Kyoichi (Kemin Japan K.K., Tokyo) ,  SHIMIZU Toshiaki (Juntendo Univ.) ,  YAMASHIRO Yuichiro (Juntendo Univ.)
Material： Congenital Anomalies  (Congenit Anom)
Volume： 48  Issue： 4  Page： 180-182  Publication year： Dec. 2008 
JST Material Number： W1431A  ISSN： 0914-3505  Document type： Article
Article type： 原著論文  Country of issue： Australia (AUS)  Language： ENGLISH (EN)

Thesaurus term： *liver disease ,...
Semi thesaurus term： *Zellweger Syndrome ,...

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JST classification (4)： Treatment for congenital diseases,deformities.  (GD03030R) ,  Drug therapy(=pharmacotherapy)for nervous system diseases  (GN05020Y) ,  Drug therapy(=pharmacotherapy)for digestive system diseases  (GH05020G) ,  Treatment for pediatric diseases.  (GC08040I)

Substance index (3)： Docosahexaenoic acid ,  Erucic acid ,  Oleic Acid

Reference (12)：

• AUGBOURG, P. A two-year trial of oleic and eruic acids ('Lorenzo's oil') as treatment for adrenomyeloneuropathy. N Engl J Med. 1993, 329, 745-752
• BOURRE, JM. Nervonic acid biosynthesis by erucyl-CoA elongation in normal and quaking mouse brain microsomes : Elongation of other unsaturated fatty acyl-CoAs (mono and poly-unsaturated). Biochim Biophys Acta. 1976, 424, 1-7
• BROWN, FR. Adrenoleukodystrophy : Effects of dietary restriction of very long chain fatty acids and of administration of carnitine and clofibrate on clinical status and plasma fatty acids. Johns Hopkins Med J. 1982, 151, 164-172
• EVRARD, P. The mechanism of arrest neuronal migration in the Zellweger malformation : An hypothesis based upon cytoarchitectonic analysis. Acta Neuropathol. 1978, 41, 109-117
• INNIS, SM. Perinatal biochemical and physiology of long-chain polyunsaturated fatty acids. J Pediatr. 2003, 143, S1-S8

Terms in the title (4)： ツェルベーガー症候群 ,  食餌 ,  ドコサヘキサエン酸 ,  治療