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J-GLOBAL ID：200902282991899038   Reference number：05A0491482

The effects of copper-histidine therapy on brain metabolism in a patient with Menkes disease: a proton magnetic resonance spectroscopic study

Menkes病患者の脳代謝に対する銅-ヒスチジン療法の効果 プロトン磁気共鳴スペクトロスコピーによる検討

Author (9)： MUNAKATA Mitsutoshi (Tohoku Univ. School of Medicine, Sendai, JPN) ,  SAKAMOTO Osamu (Tohoku Univ. School of Medicine, Sendai, JPN) ,  KITAMURA Taro (Tohoku Univ. School of Medicine, Sendai, JPN) ,  ISHITOBI Mamiko (Tohoku Univ. School of Medicine, Sendai, JPN) ,  YOKOYAMA Hiroyuki (Tohoku Univ. School of Medicine, Sendai, JPN) ,  HAGINOYA Kazuhiro (Tohoku Univ. School of Medicine, Sendai, JPN) ,  TOGASHI Noriko (Tohoku Univ. School of Medicine, Sendai, JPN) ,  KOBAYASHI Yasuko (Takuto Rehabilitation Center for Disabled Children, Sendai, JPN) ,  ONUMA Akira (Takuto Rehabilitation Center for Disabled Children, Sendai, JPN)
Material： Brain & Development  (Brain & Dev)
Volume： 27  Issue： 4  Page： 297-300  Publication year： Jun. 2005 
JST Material Number： W0814A  ISSN： 0387-7604  Document type： Article
Article type： 原著論文  Country of issue： Netherlands (NLD)  Language： ENGLISH (EN)

Thesaurus term： human(primates) ,...
Semi thesaurus term： mental retardation ,...

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JST classification (4)： Clinical application of other drugs acting on metabolism  (GW13070T) ,  Treatment for metabolic diseases,nutritional diseases.  (GD05030F) ,  Treatment for congenital diseases,deformities.  (GD03030R) ,  Drug therapy(=pharmacotherapy)for nervous system diseases  (GN05020Y)

Substance index (5)： Histidine ,  Lactic acid ,  Creatine ,  Choline ,  N-Acetylaspartic acid

Reference (10)：

• MENKES, JH. Kinky hair disease : twenty five years later. Brain Dev. 1988, 10, 77-79
• KODAMA, H. Molecular genetics and pathophysiology of Menkes disease. Pediatr Int. 1999, 41, 430-435
• CASTILLO, M. Clinical applications of proton MR spectroscopy. Am J Neuroradiol. 1996, 17, 1-15
• TSURUI, S. A pathophysiological study of macular mutant mouse as a model of human Menkes kinky hair disease. II. Analysis of brain metabolism using ^<31>P- and ^1H-nuclear magnetic resonance spectroscopy. No To Hattatsu (Tokyo). 1990, 22, 566-572
• MORGELLO, S. Menkes kinky hair disease with 'ragged red' fibers. Dev Med Child Neurol. 1988, 30, 812-816

Terms in the title (7)： Menkes病 ,  患者 ,  脳代謝 ,  銅 ,  ヒスチジン ,  療法 ,  プロトン磁気共鳴スペクトロスコピー