Art

J-GLOBAL ID：201702222627611675   Reference number：17A0578890

Heparan sulfate storage in the cardiac conduction system triggers atrioventricular block

房室ブロックを誘発する心臓刺激伝導系におけるヘパラン硫酸貯蔵

Author (10)： Kato Rie (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Kato Rie (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Miyahara Hiroaki (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Kawano Tatsuya (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Matsuzuka Atsuko (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Matsuzuka Atsuko (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Noda Kimiko (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Izumi Tatsuro (Department of Pediatrics and Child Neurology, Oita University School of Medicine, Yufu, Oita 8795593, Japan) ,  Izumi Tatsuro (Department of Pediatrics and Child Neurology, Beppu Developmental Medical Center for Cerebral Palsy, Mental Retardation and Severely Handicapped Children, Beppu, Oita 8740838, Japan) ,  Izumi Tatsuro (Department of Pediatrics and Child Neurology, Nanao National Hospital, Nanao, Ishikawa 9268531, Japan)
Material： Brain & Development  (Brain & Dev)
Volume： 39  Issue： 5  Page： 418-421  Publication year： May. 2017 
JST Material Number： W0814A  ISSN： 0387-7604  Document type： Article
Article type： 原著論文  Country of issue： Netherlands (NLD)  Language： ENGLISH (EN)

Thesaurus term： human ,...
Semi thesaurus term： *paroxysmal AV block ,...

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Author keywords (5)： Sanfilippo syndrome ,  Long-surviving patient ,  Heparan sulfate ,  Cardiac conduction system ,  Atrioventricular block

JST classification (2)： Cardiovascular system diseases  (GJ03000C) ,  Poisoning in general  (GD06010Q)

Reference (9)：

• Pyeritz, R.E. Cardiovascular manifestations of heritable disorders of connective tissue. Prog Med Genet. 1983;5:191-302.
• Kurihara, M., Kumagai, K., Yagishita, S. Sanfilippo syndrome type C: a clinicopathological autopsy study of a long-term survivor. Pediatr Neurol. 1996;14:317-21.
• Misumi, I., Chikazawa, S., Ishitsu, T., Higuchi, S., Shimazu, T., Ikeda, C. et al, Atrioventricular block and diastolic dysfunction in a patient with sanfilippo C. Int Med. 2010;49:2313-6.
• Ribeiro, E.R., Brusius-Facchin, A.C., Leistner-Segal, S., Bruno da Silva, C.A., Schwartz, I.V. Cardiac disease as the presenting feature of mucopolysaccharidosis type IIIA: a case report. Mol Genet Metab Rep. 2014;1:422-4.
• Shibata, S., Harpel, P., Bona, C., Fillit, H. Monoclonal antibodies to heparan sulfate inhibit the formation of thrombin-antithrombin III complexes. Clin Immunol Immunopathol. 1993;67:264-72.

Terms in the title (5)： 房室ブロック ,  誘発 ,  心臓刺激伝導系 ,  ヘパラン硫酸 ,  貯蔵