Art

J-GLOBAL ID：201902265285877069   Reference number：19A0494648

Altered Intracellular Milieu of ADAR2-Deficient Motor Neurons in Amyotrophic Lateral Sclerosis

筋萎縮性側索硬化症におけるADAR2欠損運動ニューロンの変化した細胞内環境【JST・京大機械翻訳】

Author (4)： Yamashita Takenari (Graduate School of Medicine, University of Tokyo, Bunkyo-ku, Tokyo 113-0033, Japan) ,  Akamatsu Megumi (Graduate School of Medicine, University of Tokyo, Bunkyo-ku, Tokyo 113-0033, Japan) ,  Kwak Shin (Graduate School of Medicine, University of Tokyo, Bunkyo-ku, Tokyo 113-0033, Japan) ,  Kwak Shin (Clinical Research Center for Medicine, International University of Health and Welfare, Ichikawa, Chiba 272-0827, Japan)
Material： Genes (Web)
Volume： 8  Issue： 2  Page： 60  Publication year： 2017 
JST Material Number： U7194A  ISSN： 2073-4425  Document type： Article
Article type： 文献レビュー  Country of issue： Switzerland (CHE)  Language： ENGLISH (EN)

Abstract/Point： Transactive response DNA-bindi...

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Thesaurus term： RNA ,  Adenosine Deaminase ,  Down-Regulation ,  pathological state ,  RNA Editing ,  *Amyotrophic Lateral Sclerosis ,  knockout mouse ,  DNA binding protein ,  pathogenesis ,  subunit ,  Phenotype ,  *motor nerve ,  AMPA receptor ,  TDP-43 ,  *ADAR2 ,  molecular genetic phenomenon ,  laboratory animal ,  Mus musculus

Author keywords (5)： amyotrophic lateral sclerosis (ALS) ,  adenosine deaminase acting on RNA 2 (ADAR2) ,  RNA editing ,  transactive response DNA-binding protein (TDP-43) ,  Ca²⁺-permeability

JST classification (1)： Basic neurology  (GN01020W)

Reference (65)：

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Terms in the title (5)： 筋萎縮性側索硬化症 ,  ADAR2 ,  欠損 ,  運動ニューロン ,  環境