Art

J-GLOBAL ID：201902229143537608   Reference number：19A0234752

Hematopoietic stem cell transplantation for progressive combined immunodeficiency and lymphoproliferation in patients with activated phosphatidylinositol-3-OH kinase δ syndrome type 1

活性化ホスファチジルイノシトール-3-OHキナーゼδ症候群1型患者における進行性複合免疫不全とリンパ増殖のための造血幹細胞移植【JST・京大機械翻訳】

Author (56)： Okano Tsubasa (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Imai Kohsuke (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Tsujita Yuki (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Mitsuiki Noriko (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Yoshida Kenichi (Department of Pathology and Tumor Biology, Graduate School of Medicine, Kyoto University, Kyoto, Japan) ,  Kamae Chikako (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Honma Kenichi (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Mitsui-Sekinaka Kanako (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Sekinaka Yujin (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Kato Tamaki (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Hanabusa Katsuyuki (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Endo Eri (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Takashima Takehiro (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Hiroki Haruka (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Yeh Tzu-Wen (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Tanaka Keisuke (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Nagahori Masakazu (Department of Gastroenterology and Hepatology, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Tsuge Ikuya (Department of Pediatrics, School of Medicine, Fujita Health University, Toyoake, Japan) ,  Bando Yuki (Department of Pediatrics, Kitasato University School of Medicine, Sagamihara, Japan) ,  Iwasaki Fuminori (Division of Hemato-Oncology Regenerative Medicine, Yokohama, Japan) ,  Shikama Yoshiaki (Division of Infectious Disease and Immunology, Kanagawa Children’s Medical Center, Yokohama, Japan) ,  Inoue Masami (Department of Hematology/Oncology, Osaka Women’s and Children’s Hospital, Osaka, Japan) ,  Kimoto Tomiko (Department of Hematology/Oncology, Osaka Women’s and Children’s Hospital, Osaka, Japan) ,  Moriguchi Naohiko (Department of Pediatrics, Kindai University Sakai Hospital, Sakai, Japan) ,  Yuza Yuki (Department of Hematology/Oncology, Tokyo Metropolitan Children’s Medical Center, Tokyo, Japan) ,  Kaneko Takashi (Department of Hematology/Oncology, Tokyo Metropolitan Children’s Medical Center, Tokyo, Japan) ,  Suzuki Kyoko (Department of Pediatrics, Juntendo University, Urayasu Hospital, Chiba, Japan) ,  Matsubara Tomoyo (Department of Pediatrics, Juntendo University, Urayasu Hospital, Chiba, Japan) ,  Maruo Yoshihiro (Department of Pediatrics, Shiga University of Medical Science, Shiga, Japan) ,  Kunitsu Tomoaki (Department of Pediatrics, Shiga University of Medical Science, Shiga, Japan) ,  Waragai Tomoko (Department of Pediatrics, Fukushima Medical University, Fukushima, Japan) ,  Sano Hideki (Department of Pediatric Oncology, Fukushima Medical University, Fukushima, Japan) ,  Hashimoto Yuko (Department of Diagnostic Pathology, Fukushima Medical University School of Medicine, Fukushima, Japan) ,  Tasaki Kazuhiro (Department of Diagnostic Pathology, Fukushima Medical University School of Medicine, Fukushima, Japan) ,  Suzuki Osamu (Department of Diagnostic Pathology, Fukushima Medical University School of Medicine, Fukushima, Japan) ,  Shirakawa Toshihiko (Department of Pediatrics, Nagasaki University Hospital, Nagasaki, Japan) ,  Kato Motohiro (Division of Transplantation and Cell Therapy, Children’s Cancer Center, National Center for Child Health and Development, Tokyo, Japan) ,  Uchiyama Toru (Department of Human Genetics, National Center for Child Health and Development, Tokyo, Japan) ,  Ishimura Masataka (Department of Pediatrics, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan) ,  Tauchi Tetsuzo (Department of Hematology, Tokyo Medical University, Tokyo, Japan) ,  Yagasaki Hiroshi (Department of Pediatrics, Nihon University Itabashi Hospital, Tokyo, Japan) ,  Jou Shiann-Tarng (Department of Pediatrics, National Taiwan University Children’s Hospital, National Taiwan University College of Medicine, Taipei, Taiwan) ,  Yu Hsin-Hui (Department of Pediatrics, National Taiwan University Children’s Hospital, National Taiwan University College of Medicine, Taipei, Taiwan) ,  Kanegane Hirokazu (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan) ,  Kracker Sven (Universite Paris Descartes, Sorbonne Paris Cite, Imagine Institute, INSERM UMR 1163, Human Lymphohematopoiesis Laboratory, Paris, France) ,  Durandy Anne (Universite Paris Descartes, Sorbonne Paris Cite, Imagine Institute, INSERM UMR 1163, Human Lymphohematopoiesis Laboratory, Paris, France) ,  Kojima Daiei (Department of Pediatrics, Nagoya University Graduate School of Medicine, Nagoya, Japan) ,  Muramatsu Hideki (Department of Pediatrics, Nagoya University Graduate School of Medicine, Nagoya, Japan) ,  Wada Taizo (Department of Pediatrics, Graduate School of Medical Science, Kanazawa University, Kanazawa, Japan) ,  Inoue Yuzaburo (Department of Pediatrics, Eastern Chiba Medical Center, Togane, Chiba, Japan) ,  Takada Hidetoshi (Department of Perinatal and Pediatric Medicine, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan) ,  Kojima Seiji (Department of Pediatrics, Nagoya University Graduate School of Medicine, Nagoya, Japan) ,  Ogawa Seishi (Department of Pathology and Tumor Biology, Graduate School of Medicine, Kyoto University, Kyoto, Japan) ,  Ohara Osamu (Department of Technology Development, Kazusa DNA Research Institute, Kisarazu, Japan) ,  Nonoyama Shigeaki (Department of Pediatrics, National Defense Medical College, Saitama, Japan) ,  Morio Tomohiro (Department of Pediatrics, Tokyo Medical and Dental University (TMDU), Tokyo, Japan)
Material： Journal of Allergy and Clinical Immunology  (J Allergy Clin Immunol)
Volume： 143  Issue： 1  Page： 266-275  Publication year： 2019 
JST Material Number： A0182B  ISSN： 0091-6749  Document type： Article
Article type： 原著論文  Country of issue： Netherlands (NLD)  Language： ENGLISH (EN)

Abstract/Point： Activated phosphatidylinositol...

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Thesaurus term： *immunologic deficiency syndrome ,  *Lymph ,  hyperplasia ,  *hematopoietic stem cell transplantation ,  graft ,  Recurrence ,  Prognosis ,  complication ,  Mutation ,  *body fluid ,  purine nucleoside ,  ribonucleoside
Semi thesaurus term： 生着不全 ,  全生存率 ,  臨床症状 ,  転帰 ,  悪性腫瘍 , 【Automatic Indexing@JST】

Author keywords (7)： Activated phosphatidylinositol-3-OH kinase δ syndrome type 1 ,  PIK3CD ,  hematopoietic stem cell transplantation ,  combined immunodeficiency ,  T-cell receptor excision circle ,  kappa-deleting recombination excision circle ,  IgG₂

JST classification (2)： Hematologic diseases  (GK03000F) ,  Immunologic diseases,allergic diseases in general.  (GD04010C)

Substance index (1)： Fludarabine

Terms in the title (9)： 活性化 ,  ホスファチジルイノシトール ,  キナーゼ ,  症候群 ,  患者 ,  複合免疫不全 ,  リンパ ,  増殖 ,  造血幹細胞移植