2021 - 2022 Investigator initiated trials to investigate the clinical response to febuxostat for aortic aneurysm in patients with Marfan syndrome.
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Papers (42):
Hiroki Yagi, Hiroshi Akazawa, Qing Liu, Kimiko Yamamoto, Kan Nawata, Akiko Saga-Kamo, Masahiko Umei, Hiroshi Kadowaki, Ryo Matsuoka, Akito Shindo, et al. XOR-Derived ROS in Tie2-Lineage Cells Including Endothelial Cells Promotes Aortic Aneurysm Progression in Marfan Syndrome. Arteriosclerosis, thrombosis, and vascular biology. 2025
Daigo Nishijo, Hiroki Yagi, Nana Akiyama, Norifumi Takeda, Masahiko Ando, Haruo Yamauchi, Norihiko Takeda, Issei Komuro. A De Novo Missense MYLK Variant Leading to Nonsyndromic Thoracic Aortic Aneurysm and Dissection Identified by Segregation Analysis. Case Reports in Genetics. 2024
Hitomi Aono-Setoguchi, Hiroki Yagi, Nana Akiyama, Norifumi Takeda, Masahiko Ando, Haruo Yamauchi, Issei Komuro, Norihiko Takeda. Management of an elderly patient with nonsyndromic TGFBR1-related aortopathy: A case report. Clinical Case Reports. 2024
Satoshi Ishii, Masaru Hatano, Shun Minatsuki, Kazutoshi Hirose, Akihito Saito, Hiroki Yagi, Mai Shimbo, Katsura Soma, Chihiro Konoeda, Masaaki Sato, et al. Comprehensive Risk Assessment in Patients With Pulmonary Arterial Hypertension Referred for Lung Transplantation. Circulation journal : official journal of the Japanese Circulation Society. 2024
New molecularly targeted therapy for prevention of aortic aneurysm progression in Marfan syndrome〜From Bench to Bedside
(The 87th Annual Scientific Meeting of the Japanese Circulation Society 2023)
Coronary periarteritis and pericardial thickening could be a predictor of coronary artery events complicated with immunoglobulin G4-related disease
(The 87th Annual Scientific Meeting of the Japanese Circulation Society 2023)